57 Even Mild Proptosis May be Pointing Towards an Underlying Massive Pial Arterio- Venous Malformation with Hydrocephalus- A Case Report & Review of the Literature

Abstract

Cerebral arterio-venous malformations tend to present most commonly with neurological manifestations like
headache, intracranial hemorrhage, seizures, or focal neurologic deficit. Intracranial vascular malformations
with aggressive imaging features manifesting only with mild unilateral proptosis are very rare with sparse
literature available on it. This report stresses upon the fact that even mild to moderate proptosis may be the
primary and solitary presenting feature of a large intracranial extra-orbital pial arterio-venous malformation
(AVM). Another feature highlighted in this case of unruptured pial arterio-venous malformation is the presence
of hydrocephalus which is secondary to extrinsic compression of the cerebral aqueduct by dilated and tortuous
draining vein.