Adenoid Cystic Carcinoma (ACC) Cervix in a Young Female- A Rare Occurrence

Abstract

Adenoid cystic carcinoma cervix (ACC) is an extremely rare (representing <1% of cervical carcinomas), highly aggressive cancer of old, macroscopically appearing as an irregular, friable mass and histologically showing a pseudo glandular or cribriform growth pattern. The tumor is highly infiltrative, often associated with vascular, lymphatic as well as perineural invasion and early recurrence. We report a case of ACC Cervix in a 20-year-old female who presented with vaginal bleeding and cervical biopsy suggested ACC. The patient underwent total abdominal hysterectomy with bilateral adnexectomy and the histopathological examination revealed adenoid cystic carcinoma cervix extending and involving endometrium and greater than 2/3rd of the myometrium with uninvolved adnexa. We report this case because of its rarity and particularly unusual occurrence in young females.