Infantile Nasal Glial Heterotopia - A Case Report

Abstract

Nasal Glial heterotopia also known as Nasal glioma is a rare, benign lesion due to defective embryonic development. It is considered to be congenital malformation of displaced normal mature, non teratomatous glial tissue without continuity with an intracranial component. The reported incidence is 1 in every 20,000 to 40,000 births. We present a case of 10-month-old infant presented to ENT department with a mass at the root of the nose since birth with gradual increase in size over months. NCCT head showed a soft tissue density mass measuring 1.8×1.8×0.2cm with no intracranial or intranasal extension. Complete surgical resection was done and specimen was sent for histopathological examination. Histopathological examination showed presence of unencapsulated mature glial tissue composed of astrocytes and fibrillary background. There were no inflammatory cells, fibrosis or calcification. Based on radiological and histopathological examination diagnosis of Nasal glioma was made. Patient had an uneventful postoperative period with no recurrence.